Npurpura trombocitopenica pdf 2013

From idiopathic to immune, the changed nomenclature is itself a testimonial to the growing awareness and improvements in the management of itp. Clinical laboratory could simplify the task of differencial diagnosis measuring adamts enzime. Immune thrombocytopenia purpura itp, also known as idiopathic thrombocytopenic purpura, is a type of thrombocytopenic purpura defined as an isolated low platelet count with a normal bone marrow in the absence of other causes of low platelets. The association between systemic lupus erythematosus sle and thrombotic thrombocytopenic purpura ttp has been infrequently reported.

Esta enfermedad afecta a varones y a mujeres por igual. Purpura trombocitopenica idiopatica busca tu medicamento. The etiopathogenic mechanisms may result from abnormalities in any of the three components of hemostasis. It is more common in women in the third and fourth decades, posible even in postpartum. Here we present a case of ttp associated to lowactivity sle. The diagnosis has always been difficult and the patients condition quickly worsens. He proposed that a powerful poison with both agglutina. Thrombocytopenic purpura is mostly responsible for episodes of mucocutaneous bleeding. A read is counted each time someone views a publication summary such as the title, abstract, and list of authors, clicks on a figure, or views or downloads the fulltext.

Pdf purpura trombocitopenica trombotica asociada a. A purpura trombocitopenica idiopatica,pti, tambem conhecida como. Usually, patients with ttp have more sle activity and frequent renal involvement. Thrombotic thrombocitopenic purpura is a rare disease with a morphological expression featured of many microthrombi in the terminal arterioles of several vital structures.

Moschcowitz was the first to inform multiple hyaline thrombi as the primordial finding of a partial autopsy case. Thrombotic thrombocytopenic purpura ttp is the most extensive and dangerous intravascular platelet clumping disorder. A practice guideline developed by explicit methods for the american society of hematology by james n. Pdf purpura trombocitopenica trombotica asociada a embarazo. Thrombotic thrombocytopenic purpura ttp is a blood disorder that results in blood clots forming in small blood vessels throughout the body. Rapid strides have been made in the field of hematology, and advances in immune thrombocytopenic purpura itp management are no exception. Purpura is a disease in which there is leakage of blood out of the blood vessels in the skin or mucosa, causing the presence of painless purplish spots, called petechiae small and large number stains or ecchymoses larger patches. Idiopathic thrombocytopenic purpura itp is diagnosed by ex clusion. In the presence of certain clinical features the possibility of an underlying vasculitic disease must be considered.

Embase foram utilizados os termos idiopathic thrombocytopenic purpuraexp e. A purpura trombocitopenica idiopatica pti, tambem conhecida como purpura. Thrombotic thrombocytopenic purpura, atypical hemolytic uremic syndrome. Purpura results from the extravasation of blood cells into the skin andor mucous membranes giving rise to small purple coloured areas that do not disappear under pressure.